Hemolytic anemia
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Etiology
Coombs positive (immune)
- Autoimmune, drugs, infection, lymphoproliferative disease, Rh or ABO incompatibility
Coombs negative
- Intrinsic red cell disease
- Abnormal hemoglobin: sickle cell disease, thalassemia, methemoglobinemia
- Membrane defect: hereditary spherocytosis, hereditary elliptocytosis, paroxysmal nocturnal hemoglobinuria
- Enzyme defect: G6PD deficiency, pyruvate kinase deficiency
- Extrinsic disease
- Microangiopathic hemolytic anemia: thrombotic thrombocytopenic purpura, hemolytic uremic syndrome, disseminated intravascular coagulation, prosthetic valve hemolysis, metastatic adenocarcinoma, vasculitis, malignant hypertension, HELLP syndrome
- Splenic sequestration
- Infection: malaria, Clostridium, Borrelia
- Burns
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Etiology
Coombs positive (immune)
- Autoimmune, drugs, infection, lymphoproliferative disease, Rh or ABO incompatibility
Coombs negative
- Intrinsic red cell disease
- Abnormal hemoglobin: sickle cell disease, thalassemia, methemoglobinemia
- Membrane defect: hereditary spherocytosis, hereditary elliptocytosis, paroxysmal nocturnal hemoglobinuria
- Enzyme defect: G6PD deficiency, pyruvate kinase deficiency
- Extrinsic disease
- Microangiopathic hemolytic anemia: thrombotic thrombocytopenic purpura, hemolytic uremic syndrome, disseminated intravascular coagulation, prosthetic valve hemolysis, metastatic adenocarcinoma, vasculitis, malignant hypertension, HELLP syndrome
- Splenic sequestration
- Infection: malaria, Clostridium, Borrelia
- Burns
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